VEPTR expansion thoracoplasty

Robert M. Campbell

Research output: Chapter in Book/Report/Conference proceedingChapter

2 Scopus citations

Abstract

Thoracic insufficiency syndrome results when deformity of the young spine and associated rib cage abnormalities cause loss of volume and function of the growing thorax, often affecting its ability to grow with the patient, with secondary compromise in growth of the underlying lungs. Disease categories most likely to cause this include fused ribs and congenital scoliosis, absence of ribs, neuromuscular or syndromic scoliosis, and hypoplastic thorax conditions such as Jeune’s asphyxiating thoracic dystrophy and Jarcho-Levin syndrome. VEPTR expansion thoracoplasties enable enlargement of the thorax in these conditions, with maintenance of gains through outpatient surgical lengthening of implanted devices, resulting in improvement in clinical pulmonary health and survival rates.

Original languageEnglish (US)
Title of host publicationThe Growing Spine
Subtitle of host publicationManagement of Spinal Disorders in Young Children, Second Edition
PublisherSpringer Berlin Heidelberg
Pages669-690
Number of pages22
ISBN (Electronic)9783662482841
ISBN (Print)9783662482834
DOIs
StatePublished - Jan 1 2015
Externally publishedYes

Keywords

  • Expansion thoracoplasty
  • Lung growth
  • Thoracic insufficiency syndrome
  • VEPTR
  • VEPTR gantry

ASJC Scopus subject areas

  • Medicine(all)

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