Two successful vaginal births after cesarean section in a patient with Hermansky-Pudlak syndrome who was treated with 1-deamino-8-arginine-vasopression during labor

Ronald D. Beesley, Randal D. Robinson, Theresa L. Stewart

Research output: Contribution to journalArticlepeer-review

10 Scopus citations

Abstract

We describe the obstetric management for a patient with Hermansky-Pudlak syndrome (HPS) and a previous cesarean delivery. The disease is characterized by oculocutaneous albinism, platelet storage dysfunction, and lipofuscin deposits in the reticuloendothelial system. Patients with the disorder are at high risk for major morbidity secondary to bleeding complications. The patient was a 22-year-old military spouse from Puerto Rico with HPS and a history of severe hemorrhage during cesarean delivery of her first child. In this report, we discuss the pathophysiologic features of HPS and the prophylactic administration of 1-deamino-8-arginine-vasopression during labor to minimize blood loss.

Original languageEnglish (US)
Pages (from-to)1048-1049
Number of pages2
JournalMilitary medicine
Volume173
Issue number10
DOIs
StatePublished - Oct 2008
Externally publishedYes

ASJC Scopus subject areas

  • Public Health, Environmental and Occupational Health

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