Transjugular Intrahepatic Portosystemic Shunt for Variceal Hemorrhage due to Recurrent of Hereditary Hemorrhagic Telangiectasia in a Liver Transplant

Marco A. Cura, Darren Postoak, Kermit V. Speeg, Rajiv Vasan

Research output: Contribution to journalArticlepeer-review

8 Scopus citations

Abstract

Hepatic involvement in hereditary hemorrhagic telangiectasia (HHT) consists of vascular malformations associated with arteriovenous (AV), arterioportal, and/or portovenous shunting. Most patients with HHT have liver involvement. Symptoms, although rare, consist of cardiac failure, pulmonary hypertension, portal hypertension, portosystemic encephalopathy, cholangitis, and atypical cirrhosis. Reported treatments for symptomatic AV malformations have been associated with substantial morbidity and mortality. This report describes a case of hepatic HHT that required liver transplantation after hepatic artery embolization. Recurrent vascular malformations developed in the transplant, resulting in portal hypertension and life-threatening variceal hemorrhage that was controlled with transjugular intrahepatic portosystemic shunt creation.

Original languageEnglish (US)
Pages (from-to)135-139
Number of pages5
JournalJournal of Vascular and Interventional Radiology
Volume21
Issue number1
DOIs
StatePublished - Jan 1 2010

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging
  • Cardiology and Cardiovascular Medicine

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