TY - JOUR
T1 - Successful management of fibrosing mediastinitis with severe vascular compromise
T2 - Report of two cases and literature review
AU - Argueta, Franklin
AU - Villafuerte, David
AU - Castaneda-Nerio, Jose
AU - Peters, Jay
AU - Restrepo, Carlos
N1 - Publisher Copyright:
© 2019
PY - 2020
Y1 - 2020
N2 - Fibrosing mediastinitis is a rare disorder characterized by the invasive proliferation of fibrous tissue within the mediastinum. This fibrosis can result in compression of intrathoracic structures including the pulmonary vasculature leading to clinical symptoms and complications like pulmonary hypertension. Here, we present two cases of young patients with fibrosing mediastinitis complicated by pulmonary artery stenosis requiring medical and endovascular management with excellent results.
AB - Fibrosing mediastinitis is a rare disorder characterized by the invasive proliferation of fibrous tissue within the mediastinum. This fibrosis can result in compression of intrathoracic structures including the pulmonary vasculature leading to clinical symptoms and complications like pulmonary hypertension. Here, we present two cases of young patients with fibrosing mediastinitis complicated by pulmonary artery stenosis requiring medical and endovascular management with excellent results.
KW - Fibrosing mediastinits
KW - Pulmonary artery stenosis
KW - Pulmonary hypertension
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U2 - 10.1016/j.rmcr.2019.100987
DO - 10.1016/j.rmcr.2019.100987
M3 - Article
C2 - 31890562
AN - SCOPUS:85076439156
SN - 2213-0071
VL - 29
JO - Respiratory Medicine Case Reports
JF - Respiratory Medicine Case Reports
M1 - 100987
ER -