Pseudomyogenic hemangioendothelioma (epithelioid sarcomalike hemangioendothelioma, fibroma-like variant of epithelioid sarcoma) of the thoracic spine

Michael McGinity, Viktor Bartanusz, Bradley Dengler, Lee Birnbaum, James Henry

Research output: Contribution to journalArticle

26 Scopus citations

Abstract

Purpose Pseudomyogenic hemangioendothelioma is a soft tissue tumor found in young adults, predominantly males. The tumor has been reported in various locations in the body, including the head, neck, chest wall, abdominal wall, genital region, and extremities. Until now, there has been no indication of occurrence in the spine. Methods A 25-year-old male presented with spinal cord compression, due to an extradural tumor involving the third and fourth thoracic vertebrae with extension into the right pleural cavity. Results Histopathologic examination revealed a pseudomyogenic hemangioendothelioma, also described as epithelioid sarcoma-like hemangioendothelioma, orfibroma-like variant of epithelioid sarcoma. Conclusion We describe the first occurrence of pseudomyogenic hemangioendothelioma in the thoracic spine. According to previous reports based on other locations, the tumor has an indolent clinical course with a small risk of metastasis, therefore complete macroscopic excision is the treatment of choice. Local recurrence may occur even with complete surgical resection, requiring close follow-up; adjuvant therapy is warranted.

Original languageEnglish (US)
Pages (from-to)S506-S511
JournalEuropean Spine Journal
Volume22
Issue numberSUPPL.3
DOIs
StatePublished - May 1 2013

Keywords

  • Epithelioid sarcoma-like hemangioendothelioma
  • Fibroma-like variant of epithelioid sarcoma
  • Pseudomyogenic hemangioendothelioma
  • Thoracic spine tumor

ASJC Scopus subject areas

  • Surgery
  • Orthopedics and Sports Medicine

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