Laparoscopic treatment of accessory ureterocele in a patient with müllerian aplasia

Müllerian aplasia is characterized by incomplete development of müllerian ducts into tubes, uterus, and upper vagina. This syndrome is frequently associated with urinary tract abnormalities, including renal agenesis or ectopia and accessory ureter. We describe a 16-year-old female with primary amenorrhea and a diagnosis of müllerian aplasia. Pelvic ultrasound examination revealed a left-sided cystic pelvic mass. MRI revealed normal kidneys, calyces, and ureters with a cystic left adnexal mass. During laparoscopy, this mass was found to be an accessory ureter with ureterocele. The ureterocele and accessory ureter were laparoscopically resected. The ureterocele sac contained multiple calculi. Diagnosis and laparoscopic management of this rare anomaly are described.