Congenital absence of the pulmonary valve associated with congenital aplasia of the thymus (DiGeorge's syndrome)

J. S. Rose, D. C. Levin, S. Goldstein, W. Laster

Research output: Chapter in Book/Report/Conference proceedingChapter

15 Citations (Scopus)

Abstract

Two cases of DiGeorge's syndrome associated with tetralogy of Fallot and absence of the pulmonic valve are reported. Both infants had complete absence of the thymus and parathyroids. This brings to a total of 4 the number of reported cases of absence of the pulmonic valve in this rare syndrome. Some of the expected roentgen signs, such as a narrow mediastinal silhouette and marked enlargement of the central pulmonary arteries, may be masked by cardiomediastinal shift due to bronchial compression. The angiographic findings are discussed.

Original languageEnglish (US)
Title of host publicationAMER.J.ROENTGENOL.
Pages97-102
Number of pages6
Volume122
Edition1
StatePublished - 1974
Externally publishedYes

Fingerprint

DiGeorge Syndrome
Pulmonary Valve
Thymus Gland
Lung
Tetralogy of Fallot
Pulmonary Artery

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Rose, J. S., Levin, D. C., Goldstein, S., & Laster, W. (1974). Congenital absence of the pulmonary valve associated with congenital aplasia of the thymus (DiGeorge's syndrome). In AMER.J.ROENTGENOL. (1 ed., Vol. 122, pp. 97-102)

Congenital absence of the pulmonary valve associated with congenital aplasia of the thymus (DiGeorge's syndrome). / Rose, J. S.; Levin, D. C.; Goldstein, S.; Laster, W.

AMER.J.ROENTGENOL.. Vol. 122 1. ed. 1974. p. 97-102.

Research output: Chapter in Book/Report/Conference proceedingChapter

Rose, JS, Levin, DC, Goldstein, S & Laster, W 1974, Congenital absence of the pulmonary valve associated with congenital aplasia of the thymus (DiGeorge's syndrome). in AMER.J.ROENTGENOL.. 1 edn, vol. 122, pp. 97-102.
Rose JS, Levin DC, Goldstein S, Laster W. Congenital absence of the pulmonary valve associated with congenital aplasia of the thymus (DiGeorge's syndrome). In AMER.J.ROENTGENOL.. 1 ed. Vol. 122. 1974. p. 97-102
Rose, J. S. ; Levin, D. C. ; Goldstein, S. ; Laster, W. / Congenital absence of the pulmonary valve associated with congenital aplasia of the thymus (DiGeorge's syndrome). AMER.J.ROENTGENOL.. Vol. 122 1. ed. 1974. pp. 97-102
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