Acquired right ventricular outflow obstruction in a child with neurofibromatosis

Glenn C. Rosenquist; L. Jerome Krovetz; J. Alex Haller; Allan L. Simon; George A. Bannayan

doi:10.1016/0002-8703(70)90399-6

Acquired right ventricular outflow obstruction in a child with neurofibromatosis

Glenn C. Rosenquist, L. Jerome Krovetz, J. Alex Haller, Allan L. Simon, George A. Bannayan

Research output: Contribution to journal › Article › peer-review

15 Scopus citations

Abstract

A case of severe acquired localized right ventricular obstruction in an 8 1 2-year-old child with von Recklinghausen's syndrome is presented. The similarity of this case to vascular involvement in previously reported cases is pointed out. It is suggested that vascular lesions in neurofibromatosis may have varied manifestations and that this syndrome should be thought of in the future as a generalized disease which may affect any part of the cardiovascular system. For the lesion here reported, excision of the fibromuscular band has resulted in disappearance of her pressure difference, murmur, and right heart failure.

Original language	English (US)
Pages (from-to)	103-108
Number of pages	6
Journal	American Heart Journal
Volume	79
Issue number	1
DOIs	https://doi.org/10.1016/0002-8703(70)90399-6
State	Published - Jan 1970
Externally published	Yes

ASJC Scopus subject areas

Cardiology and Cardiovascular Medicine

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10.1016/0002-8703(70)90399-6

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title = "Acquired right ventricular outflow obstruction in a child with neurofibromatosis",

abstract = "A case of severe acquired localized right ventricular obstruction in an 8 1 2-year-old child with von Recklinghausen's syndrome is presented. The similarity of this case to vascular involvement in previously reported cases is pointed out. It is suggested that vascular lesions in neurofibromatosis may have varied manifestations and that this syndrome should be thought of in the future as a generalized disease which may affect any part of the cardiovascular system. For the lesion here reported, excision of the fibromuscular band has resulted in disappearance of her pressure difference, murmur, and right heart failure.",

author = "Rosenquist, {Glenn C.} and Krovetz, {L. Jerome} and Haller, {J. Alex} and Simon, {Allan L.} and Bannayan, {George A.}",

note = "Funding Information: From the Departments of Pediatrics. Surgery. Radiology, and Pathology. The Johns Hopkins University Medicine. and the Children{\textquoteright}s Medical and Surgical Center. The Johns Hopkins Hospital, Baltimore, This work was aided by Grant HE-10191-03 from the National Institutes of Health. Received for publication Jan. 23, 1969. *Recipient of a Research Career Development **Recipient of Research Career Development",

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doi = "10.1016/0002-8703(70)90399-6",

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T1 - Acquired right ventricular outflow obstruction in a child with neurofibromatosis

AU - Rosenquist, Glenn C.

AU - Krovetz, L. Jerome

AU - Haller, J. Alex

AU - Simon, Allan L.

AU - Bannayan, George A.

N1 - Funding Information: From the Departments of Pediatrics. Surgery. Radiology, and Pathology. The Johns Hopkins University Medicine. and the Children’s Medical and Surgical Center. The Johns Hopkins Hospital, Baltimore, This work was aided by Grant HE-10191-03 from the National Institutes of Health. Received for publication Jan. 23, 1969. *Recipient of a Research Career Development **Recipient of Research Career Development

PY - 1970/1

Y1 - 1970/1

N2 - A case of severe acquired localized right ventricular obstruction in an 8 1 2-year-old child with von Recklinghausen's syndrome is presented. The similarity of this case to vascular involvement in previously reported cases is pointed out. It is suggested that vascular lesions in neurofibromatosis may have varied manifestations and that this syndrome should be thought of in the future as a generalized disease which may affect any part of the cardiovascular system. For the lesion here reported, excision of the fibromuscular band has resulted in disappearance of her pressure difference, murmur, and right heart failure.

AB - A case of severe acquired localized right ventricular obstruction in an 8 1 2-year-old child with von Recklinghausen's syndrome is presented. The similarity of this case to vascular involvement in previously reported cases is pointed out. It is suggested that vascular lesions in neurofibromatosis may have varied manifestations and that this syndrome should be thought of in the future as a generalized disease which may affect any part of the cardiovascular system. For the lesion here reported, excision of the fibromuscular band has resulted in disappearance of her pressure difference, murmur, and right heart failure.

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Acquired right ventricular outflow obstruction in a child with neurofibromatosis

Abstract

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